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中华临床医师杂志(电子版) ›› 2023, Vol. 17 ›› Issue (07) : 838 -843. doi: 10.3877/cma.j.issn.1674-0785.2023.07.014

病例报告

腹盆腔巨大多发黏液乳头型室管膜瘤合并肠梗阻一例
林寅, 高仁元, 夏凯, 吴小材, 孙静, 尹路, 陈春球()   
  1. 200072 上海,同济大学附属第十人民医院腹部外科疑难诊治中心
  • 收稿日期:2022-07-05 出版日期:2023-07-15
  • 通信作者: 陈春球

Giant multiple myxopapillary ependymomas in the abdomen and pelvis complicated with intestinal obstruction: a case report

Yin Lin, Renyuan Gao, Kai Xia   

  • Received:2022-07-05 Published:2023-07-15
引用本文:

林寅, 高仁元, 夏凯, 吴小材, 孙静, 尹路, 陈春球. 腹盆腔巨大多发黏液乳头型室管膜瘤合并肠梗阻一例[J]. 中华临床医师杂志(电子版), 2023, 17(07): 838-843.

Yin Lin, Renyuan Gao, Kai Xia. Giant multiple myxopapillary ependymomas in the abdomen and pelvis complicated with intestinal obstruction: a case report[J]. Chinese Journal of Clinicians(Electronic Edition), 2023, 17(07): 838-843.

图1 影像学资料。图a为横断位显示肿瘤广泛浸润盆腔;图b为矢状位未见肿瘤椎管内累及;图c为冠状位显示腹膜后及骶前区巨大肿瘤
图2 手术视频图。图a为腹腔镜探查发现大网膜结节;图b为发现乙状结肠后方巨大肿瘤;图c为开腹取出肿瘤;图d为离断直肠及乙状结肠;图e为腹膜后肿瘤剥除;图f为俯卧位切除骶尾部后方肿瘤;图g为S2以下切除骶尾骨;图h为骶前肿瘤切除
图3 黏液乳头型室管膜瘤病理标本。图a为肿瘤及骶尾骨切除术后大体标本;图b为肿瘤组织切片HE染色;图c为CD56(+);图d为S-100(+);图e为Vimentin(+);图f为P53(+++);图g为GFAP(+);图h为EMA(+);图i为Ki67(5%);图j为Olig-2(+);图k为CK-P(-);图l为BRAC(-)
表1 室管膜瘤的鉴别诊断(2021WHO第五版分类)
表2 MPEs的鉴别诊断
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